Note: Because of the diversity of topics under this heading, the articles chosen here are review articles which provide references to other important articles for the topic that they address.

RBC membrane disorders - general

Tse WT, Lux SE.

Red Blood Cell Membrane Disorders.
British Journal of Hematology, 1999, 104: 2-13.
PubMed citation number: 10027705

Delaunay J.

Molecular basis of red cell membrane disorders.
Acta Haematol. 2002;108:210
PubMed citation number: 12432217

Mohandas N, Gascard P.

What do mouse gene knockouts tell us about the structure and function of the red cell membrane?
Baillieres Best Pract Res Clin Haematol. 2001;14:835
PubMed citation number: 10895255

Mohandas N, Chasis JA.

Red blood cell deformability, membrane material properties and shape: regulation by transmembrane, skeletal and cytosolic proteins and lipids.
Semin Hematol. 1993;30:171
PubMed citation number: 8211222

Hereditary spherocytosis

Chasis JA, Agre P, Mohandas N.

Decreased membrane mechanical stability and in vivo loss of surface area reflect spectrin deficiencies in hereditary spherocytosis.
J Clin Invest 1988;82:617
PubMed citation number: 3403720

Da Costa L, Mohandas N, Sorette M, Grange MJ, Tchernia G, Cynober T.

Temporal differences in membrane loss lead to distinct reticulocyte features in hereditary spherocytosis and in immune hemolytic anemia.
Blood 2001;98:2894
PubMed citation number: 11698268

Bader-Meunier B. Gauthier F. Archambaud F. Cynober T. Mielot F. Dommergues

JP. Warszawski J. Mohandas N. Tchernia G.
Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis.
Blood. 2001 97(2): 399-403.
PubMed citation number: 11154215

Hereditary elliptocytosis / pyropoikilocytosis

Hanspal M et al.

Molecular basis of spectrin deficiency in hereditary pyropoikilocytosis.
Blood 1993;82:1652
PubMed citation number: 8364214

Hereditary stomatocytosis

Delaunay J, Stewart G, Iolascon A.

Hereditary dehydrated and overhydrated stomatocytosis: recent advances.
Current Opinion in Hematology, 1999, 6(2): 110-4.
PubMed citation number: 10088641

Acanthocytosis

Biemer JJ.

Acanthocytosis—biochemical and physiological considerations.
Annals of Clinical and Laboratory Science. 1980, 10(3): 238-49.
PubMed citation number: 6994580

Rh deficiency syndrome

Ballas SK, Clark MR, Mohandas N, Colfer HF, Caswell MS, Bergren MO, Perkins

HA, Shohet SB. Red cell membrane and cation deficiency in Rh null syndrome.
Blood 1984; 63:1046
PubMed citation number: 6324926

Cartron JP.

RH blood group system and molecular basis of Rh-deficiency.
Baillieres Best Pract Res Clin Haematol. 1999 Dec;12(4):655-8
PubMed citation number: 10895258

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